Chapter Eighteen, part 1

We are a bit slappy at the beginning of the episode since we had just recorded our conversation with the Glaucomfleckens.

References

Chapter 18 Metabolic alkalosis! 

Part 1 February 23, 2023

  1. It is chloride depletion alkalosis, not contraction alkalosis classic review by Galla and Luke, the metabolic alkalosis mavens who review the role of chloride.

  2. On the mechanism by which chloride corrects metabolic alkalosis in man and this is the study when they induced a metabolic alkalosis and studied the effect of treating with KCl vs NaPhos and found the former (with chloride) reversed the alkalosis but not the sodium containing protocol. 

  3. Some elegant reports on the increased proximal reabsorption of bicarbonate above normal stimulated by Ang II. 

    1. Tubular transport responses to angiotensin | American Journal of Physiology-Renal Physiology

    2. Crosstalk between the renal sympathetic nerve and intrarenal angiotensin II modulates proximal tubular sodium reabsorption - Pontes - 2015 - Experimental Physiology - Wiley Online Library

  4. THE RENAL REGULATION OF ACID-BASE BALANCE IN MAN. III. THE REABSORPTION AND EXCRETION OF BICARBONATE 1949  this is the correct figure for 11.14 and shows what happens when filtered bicarb exceeds normal threshold in normal human (men) and appears in the urine. 

  5. Masterful review Symposium on acid-base homeostasis. The generation and maintenance of metabolic alkalosis by Seldin and Rector 

  6. And a modern review from Michael Emmet! Metabolic Alkalosis - PMC (so many favorite reviews on this exciting topic!) and this one from Soleimani Metabolic Alkalosis Pathogenesis, Diagnosis, and Treatment: Core Curriculum 2022 both of these elaborate on pendrin’s role. 

  7. The effect of prolonged administration of large doses of sodium bicarbonate in man  (Clin Sci. 1954 Aug;13(3):383-401)

  8. Kidney v Renal: KDIGO versus Don’t

Plus: We got a little off topic and discussed the Kidney Failure Risk Equation: https://kidneyfailurerisk.com/

Outline: Chapter 18 Metabolic Alkalosis

  • Elevation of arterial pH, increased plasma HCO3, and compensatory hypoventilation

    • High HCO3 may be compensatory for respiratory acidosis

    • HCO3 > 40 indicates metabolic alkalosis

  • Pathophysiology: Two Key Questions

    • How do patients become alkalotic?

    • Why do they remain alkalotic?

  • Generation of Metabolic Alkalosis

    • Loss of H+ ions

      • GI loss: vomiting, GI suction, antacids

      • Renal loss: diuretics, mineralocorticoid excess, hypercalcemia, post-hypercapnia

    • Administration of bicarbonate

    • Transcellular shift

      • K+ loss → H+ shifts intracellularly

      • Intracellular acidosis

      • Refeeding syndrome

    • Contraction alkalosis

      • Same HCO3, smaller extracellular volume → increased [HCO3]

      • Seen in CF (sweating), illustrated in Fig 18-1

    • Common theme: hypochloremia is essential for maintenance

  • Maintenance of Metabolic Alkalosis

    • Kidneys normally excrete excess HCO3

      • Example: Normal subjects excrete 1000 mEq NaHCO3/day with minor pH change

    • Impaired HCO3 excretion required for maintenance

      • Table 18-2

    • Mechanisms of Maintenance

      • Decreased GFR (less important)

      • Increased tubular reabsorption

        • Proximal tubule (PT): reabsorbs 90% of filtered HCO3

        • TALH and distal nephron manage the rest

        • Contributing factors:

          • Effective circulating volume depletion

            • Enhances HCO3 reabsorption

            • Ang II increases Na-H exchange

            • Increased tubular [HCO3] enables more H+ secretion

          • Distal nephron HCO3 reabsorption

            • Stimulated by aldosterone (↑ H-ATPase, ↑ Na reabsorption)

              • Negative luminal charge impedes H+ back-diffusion

          • Chloride depletion

            • Reduces NaK2Cl activity → ↑ renin → ↑ aldosterone

            • Luminal H-ATPase co-secretes Cl → low Cl increases H+ secretion

            • Cl-HCO3 exchanger needs Cl gradient → low Cl impairs HCO3 secretion

          • Key conclusion: Cl depletion > volume depletion in perpetuating alkalosis

            • Albumin corrects volume but not alkalosis

            • Non-N Cl salts correct alkalosis without fixing volume

    • Hypokalemia

      • Stimulates H+ secretion and HCO3 reabsorption

        • Transcellular shift (H/K exchange) → intracellular acidosis

        • H-K ATPase reabsorbs K and secretes H

        • Severe hypokalemia reduces Cl reabsorption → ↑ H+ secretion

      • Important with mineralocorticoid excess

  • Respiratory Compensation

    • Hypoventilation: 0.7 mmHg PCO2 ↑ per 1 mEq/L HCO3 ↑

    • PCO2 can exceed 60

    • Rise in PCO2 increases acid excretion (limited effect on pH)

  • Epidemiology

    • GI Hydrogen Loss

      • Gastric juice: high HCl, low KCl

      • Stomach H+ generation → blood HCO3

        • Normally recombine in duodenum

        • Vomiting/antacids prevent recombination → alkalosis

      • Antacids (e.g., MgOH)

        • Mg binds fats, leaves HCO3 unbound → alkalosis

        • Renal failure impairs excretion

      • Cation exchange resins (SPS, MgCO3) → same effect

      • Congenital chloridorrhea

        • High fecal Cl-, low pH → metabolic alkalosis

        • PPI may help by reducing gastric Cl load

    • Renal Hydrogen Loss

      • Mineralocorticoid excess & hypokalemia

        • Aldosterone → H+ ATPase stimulation, Na+ reabsorption → negative lumen → ↑ H+ secretion

      • Diuretics (loop/thiazide)

        • Volume contraction

        • Secondary hyperaldosteronism

        • Increased distal flow and H+ loss

      • Posthypercapnic alkalosis

        • Chronic respiratory acidosis → ↑ HCO3

        • Rapid correction (ventilation) → unopposed HCO3 → alkalosis

        • Gradual CO2 correction needed

        • Maintenance: hypoxemia, Cl loss

      • Low chloride intake (infants)

        • Na+ reabsorption must exchange with H+/K+

        • H+ co-secretion with Cl impaired if Cl is low

      • High dose carbenicillin

        • High Na+ load without Cl

        • Nonresorbable anion → hypokalemia, alkalosis

      • Hypercalcemia

        • ↑ Renal H+ secretion & HCO3 reabsorption

        • Can contribute to milk-alkali syndrome

        • Rarely causes acidosis via reduced proximal HCO3 reabsorption

    • Intracellular H+ Shift

      • Hypokalemia

        • Common cause and effect of metabolic alkalosis

        • H+/K+ exchange → intracellular acidosis → ↑ H+ excretion

      • Refeeding Syndrome

        • Rapid carb reintroduction → cellular shift

        • No volume contraction or acid excretion increase

    • Retention of Bicarbonate

      • Requires impaired excretion to become significant

      • Organic anions (lactate, acetate, citrate, ketoacids)

        • Metabolism → CO2 + H2O + HCO3

        • Citrate in blood transfusion (16.8 mEq/500 mL)

          • 8 units → alkalosis risk

      • CRRT + citrate anticoagulant

      • Sodium bicarbonate therapy

        • Rebound alkalosis possible with acid reversal (e.g., ketoacidosis)

        • Extreme cases: pH up to 7.9, HCO3 up to 70

    • Contraction Alkalosis

      • NaCl and water loss without HCO3

      • Seen in vomiting, diuretics, CF sweat

      • Mild losses neutralized by intracellular buffers

  • Symptoms

    • Often asymptomatic

    • From volume depletion: dizziness, weakness, cramps

    • From hypokalemia: polyuria, polydipsia, weakness

    • From alkalosis (rare): paresthesias, carpopedal spasm, lightheadedness

      • More common in respiratory alkalosis due to rapid pH shift across BBB

    • Physical exam not usually helpful

      • Clues: signs of vomiting

  • Diagnosis

    • History is key

      • If unclear, suspect:

        • Surreptitious vomiting

        • CF

        • Secret diuretic use

        • Mineralocorticoid excess

    • Use urine chloride

      • Table 18-3: urine Na is misleading in alkalosis

      • Table 18-4: urine chemistry changes with complete HCO3 reabsorption

        • Vomiting: low urine Na, K, Cl + acidic urine

        • Sufficient NaCl intake prevents this stage

        • Exceptions to low urine Cl:

          • Severe hypokalemia

          • Tubular defects

          • CKD

    • Distinguishing from respiratory acidosis

      • Use pH as guide

      • Caution with typo (duplicate pCO2)

      • A-a gradient might help

  • Treatment

    • Correct K+ and Cl− deficiency → kidneys self-correct

    • Upper GI losses: add H2 blockers

    • Saline-responsive alkalosis

      • Treat with NaCl

      • Mechanisms:

        • Reverse contraction component

        • Reduce Na+ retention → promote NaHCO3 excretion

        • ↑ distal Cl delivery → enable HCO3 secretion via pendrin

      • Monitor urine pH: from 5.5 → 7–8 with therapy

      • Give K+ with Cl, not phosphate, acetate, or bicarbonate

    • Saline-resistant alkalosis

      • Seen in edematous states or K+ depletion

        • Edema (CHF, cirrhosis): use acetazolamide, HCl, dialysis

          • Acetazolamide: may ↑ CO2 via RBC carbonic anhydrase inhibition

        • Mineralocorticoid excess: K+ + K-sparing diuretic (use caution)

        • Severe hypokalemia:

          • eNaC Na+ reabsorption must be countered by H+ if no K+

          • Corrects rapidly with K+ replacement

          • Restores saline responsiveness

        • Renal failure: requires dialysis